Full Description
Aim of this publication is to offer readers a comprehensive surgical textbook that addresses exclusively rare liver and biliary diseases in pediatric and adult populations.
It will explain the origin of these types of diseases and provide guidance about their clinical manifestation, diagnosis, and treatment options. State-of-the-art research in the areas will be presented.
Written by a multidisciplinary team of world-known experts in the field addressing the knowledge gap about these rare diseases - many medical professionals, specialists as well as general practitioners, are unfamiliar with these diseases due to their rarity. This textbook will therefore target medical clinicians, including medical students and residents, PhD students, and post-docs. Multiple specialties (oncology, surgery, pediatrics, endocrinology) will find the book a valuable resource.
Contents
Chapter 1- Allagile's syndrome.- Chapter 2-Traumatic and post-surgical biliary tract diseases.- Chapter 3-Epithelioid hemangioendothelioma.- Chapter 4-Liver fluke.- Chapter 5-Mucinous cystic neoplasms.- Chapter 6- Embryologic rare liver tumors.- Chapter 7 Hepatobiliary Sarcoma.- Chapter 8-Caroli disease.- Chapter 9-Cryptogenic cirrhosis.- Chapter 10-Wilson's disease.- Chapter 11-Hemochromatosis.- Chapter 12- Biliary atresia.- Chapter 13-Alpha-1 antitrypsin deficiency.- Chapter 14-Cirrhosis secondary to prolonged total parental nutrition.- Chapter 15-Echinococcus.- Chapter 16-Fibrolamellar hepatocellular carcinoma (FL-HCC).- Chapter 17-Mesenchymal hamartoma.- Chapter 18-Intraductal papillary mucinous neoplasm of the biliary tract (IPMN-B).- Chapter 19-Extrahepatic biliary atresia.- Chapter 20-Hepatoblastoma.- Chapter 21-Congenital hepatic fibrosis.- Chapter 22-Budd Chiarri.- Chapter 23-Urea cycle deficiency.- Chapter 24-Mitochondrial disorders.- Chapter 25- Navajo neurohepatopathy.- Chapter 26-Familial intra-hepatic cholestasis (Byler disease).- Chapter 27-Obstructive biliary tract disease.- Chapter 28-Choledochal cysts.- Chapter 29-Pregnancy and liver diseases.- Chapter 30-Rare benign hepatic cysts.- Chapter 31-Maple Syrup Urine diseases.- Chapter 32-Primary sclerosing cholangitis.- Chapter 33-Inflammatory pseudotumors.
