Full Description
The second edition comprehensively reviews the wide field of rare pulmonary diseases. Issues such as less common diseases affecting the airways, systematic disorders with lung involvement, interstitial lung diseases, and many other orphan conditions of the lungs are explored in this book. The progress and advances made in the field and the limited number of patients presenting each condition makes it very difficult for clinicians to be up-to-date in this field. Readers will discover how to diagnose and manage these rare orphan diseases. Orphan Lung Diseases: A Clinical Guide to Rare Lung Disease is a practical, informative book written by a team of international authors with much experience in rare pulmonary diseases
Orphan Lung Diseases: A Clinical Guide to Rare Lung Disease, second edition provides synthesized and easily accessible information about the main orphan lung diseases, to aid clinicians in charge of patients with rare disease,or who consider the diagnosis of a rare disease in their patient. It is a practical, informative guide written by a team of international experienced authors in rare pulmonary diseases.
Contents
Chapter 1. Orphan lung diseases: from definition to organisation of care.-Chapter 2. The challenge of clinical research in orphan diseases.- Chapter 3. Chronic bronchiolitis in adults.- Chapter 4. Allergic bronchopulmonary mycosis.- Chapter 5. Orphan tracheopathies.- Chapter 6. Amyloidosis of the lungs and airways.- Chapter 7. Eosinophilic granulomatosis with polyangiitis.- Chapter 8. Granulomatosis with polyangiitis.- Chapter 9. Alveolar hemorrhage.- Chapter 10. Pulmonary manifestations of large vessel vasculitis (Behçet and Takayasu disease) .- Chapter 11. Hepato-pulmonary syndrome.- Chapter 12. Systemic sclerosis and the lung.- Chapter 13. Rheumatoid arthritis and the lung.- Chapter 14. Lung disease in systemic lupus erythematosus, myositis, Sjögren disease and mixed connective tissue diseases.- Chapter 15. Interstitial pneumonia with autoimmune features, and overlap interstitial pneumonia.- Chapter 16. Non-Langerhans cell histiocytosis and the lung.- Chapter 17. Idiopathic eosinophilic pneumonias.- Chapter 18. Langerhans cell granulomatosis and smoking-related interstitial lung diseases.- Chapter 19. Lymphangioleiomyomatosis.- Chapter 20. Multiple cystic lung disease.- Chapter 21. Complex Thoracic Lymphatic Disorders of Adults.- Chapter 22. Pulmonary alveolar proteinosis.- Chapter 23. Gasteroesosophageal reflux, idiopathic pulmonary fibrosis and lung transplantation.- Chapter 24. Genetic and familial pulmonary fibrosis related to monogenic diseases.- Chapter 25. Diffuse bronchiectasis of genetic or idiopathic origin.- Chapter 26. Pulmonary vascular manifestations of hereditary hemorrhagic telangiectasia.- Chapter 27. Pulmonary alveolar microlithiasis.- Chapter 28. Rare diffuse lung diseases of genetic origin.- Chapter 29. Imaging approach to interstitial lung disease.- Chapter 30. Bronchoscopic approach to interstitial lung disease.- Chapter 31. An integrated approach to diagnosing interstitial lung disease.- Chapter 32. Idiopathic Pulmonary fibrosis and the many faces of UIP.- Chapter 33. Combined pulmonary fibrosis and emphysema (syndrome) .- Chapter 34. Nonspecific interstitial pneumonia, idiopathic or secondary.- Chapter 35. Organising pneumonias and acute interstitial pneumonia.- Chapter 36. Pleuro pulmonary fibroelastosis.- Chapter 37.Interstitial lung diseases of occupational origin.- Chapter 38. Unclassifiable Interstitital Lung Disease.- Chapter 39. Lymphoproliferative lung diseases.- Chapter 40. Pulmonary manifestations of hematological malignancies and recipients of bone marrow or stem cell transplantation.- Chapter 41. Pulmonary hypertension in orphan lung diseases.- Chapter 42. Drug-induced / iatrogenic respiratory disease: With emphasis on unusual, rare and emergent drug-induced reactions.- Chapter 43. Malignant mimics of orphan lung diseases.
