Description
In this issue of Clinics in Chest Medicine, guest editors Drs. Cormac McCarthy and Nishant Gupta bring their considerable expertise to the topic of Rare and Orphan Lung Diseases. Top experts discuss both rare and orphan diseases (those which are not widely researched, those where specific treatments are not available, and those which may only be of limited interest to scientists and doctors). Topics in this issue include primary ciliary dyskinesia, multiple cystic lung diseases, and idiopathic eosinophilic pneumonias.- Contains 17 relevant, practice-oriented topics including lymphangioleiomyomatosis; pulmonary Langerhans cell histiocytosis; Birt Hogg Dube syndrome; lymphatic disorders and the lung; plmonary vasculitis; antisynthetase syndromes; monogenic familial ILD; Hermansky Pudlak syndrome; and more- Provides in-depth clinical reviews on rare and orphan lung diseases, offering actionable insights for clinical practice- Presents the latest information on this timely, focused topic under the leadership of experienced editors in the field. Authors synthesize and distill the latest research and practice guidelines to create clinically significant, topic-based reviews
Table of Contents
Current Perspectives on The Diagnosis and Management of LymphangioleiomyomatosisPulmonary Langerhans Cell HistiocytosisBirt–Hogg–Dube´ SyndromePulmonary Alveolar ProteinosisPulmonary Alveolar Microlithiasis: A Disorder of Pulmonary Phosphate HomeostasisEosinophilic Lung DiseasesGenetic Familial Interstitial Lung DiseaseHermansky-Pudlak SyndromeAmyloid and Light Chain Deposition DisordersNeuroendocrine Hyperplasia of Infancy and Diffuse Idiopathic Neuroendocrine Cell Hyperplasia: Two Faces of Pulmonary Neuroendocrine Cell PathologyPulmonary Manifestations of Lysosomal Storage Disorders in Adults
